Een letale blaarvormende auto-immuunziekte

Translated title of the contribution: A lethal blistering autoimmune disease

M. Aniek Lamberts*, G. F.H. Diercks, K. de Leeuw, J. M. Meijer

*Corresponding author for this work

Research output: Contribution to journalArticleAcademicpeer-review

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Abstract

Dermatomyositis is an autoimmune disease characterized by chronic inflammation of skin and muscle. Anti-melanoma differentiation-associated gene 5 (MDA5) associated dermatomyositis is a recently described variant that displays a unique dermatological phenotype consisting of punched-out cutaneous ulcers, palmar erythema, papules or blisters at typical sites of dermatomyositis. Moreover, anti-MDA5 associated dermatomyositis patients have an increased risk to develop a rapidly progressive interstitial lung disease with a potentially fatal course. Cutaneous ulcers are an important predictor for the development of interstitial lung disease. We report an illustrative case of anti-MDA5 associated dermatomyositis.

Translated title of the contributionA lethal blistering autoimmune disease
Original languageDutch
Pages (from-to)36-38
Number of pages3
JournalNederlands Tijdschrift voor Dermatologie en Venereologie
Volume31
Issue number6
Publication statusPublished - Jun-2021

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