Energy expenditure in patients with propionic and methylmalonic acidaemias

C C van Hagen; E Carbasius Weber; Th A M van den Hurk; J H Oudshoorn; L Dorland; R Berger; T de Koning

doi:10.1023/B:BOLI.0000016678.78134.7d

Energy expenditure in patients with propionic and methylmalonic acidaemias

C C van Hagen, E Carbasius Weber, Th A M van den Hurk, J H Oudshoorn, L Dorland, R Berger, T de Koning

Research output: Contribution to journal › Article › Academic › peer-review

11 Citations (Scopus)

Abstract

Resting energy expenditure (REE) was investigated in 8 children with propionic and methylmalonic acidaemias because a lowered REE has been reported in the literature. We observed a marginally elevated REE and think that adequate caloric intake and the use of a synthetic amino acid mixture are responsible for this.

Original language	English
Pages (from-to)	111-112
Number of pages	2
Journal	Journal of Inherited Metabolic Disease
Volume	27
Issue number	1
DOIs	https://doi.org/10.1023/B:BOLI.0000016678.78134.7d
Publication status	Published - 2004
Externally published	Yes

Keywords

Amino Acid Metabolism, Inborn Errors
Amino Acids
Child
Child, Preschool
Drug Combinations
Energy Intake
Energy Metabolism
Female
Humans
Infant
Male
Methylmalonic Acid
Propionates
Journal Article

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title = "Energy expenditure in patients with propionic and methylmalonic acidaemias",

abstract = "Resting energy expenditure (REE) was investigated in 8 children with propionic and methylmalonic acidaemias because a lowered REE has been reported in the literature. We observed a marginally elevated REE and think that adequate caloric intake and the use of a synthetic amino acid mixture are responsible for this.",

keywords = "Amino Acid Metabolism, Inborn Errors, Amino Acids, Child, Child, Preschool, Drug Combinations, Energy Intake, Energy Metabolism, Female, Humans, Infant, Male, Methylmalonic Acid, Propionates, Journal Article",

author = "{van Hagen}, {C C} and {Carbasius Weber}, E and {van den Hurk}, {Th A M} and Oudshoorn, {J H} and L Dorland and R Berger and {de Koning}, T",

year = "2004",

doi = "10.1023/B:BOLI.0000016678.78134.7d",

language = "English",

volume = "27",

pages = "111--112",

journal = "Journal of Inherited Metabolic Disease",

issn = "0141-8955",

publisher = "Springer",

number = "1",

}

TY - JOUR

T1 - Energy expenditure in patients with propionic and methylmalonic acidaemias

AU - van Hagen, C C

AU - Carbasius Weber, E

AU - van den Hurk, Th A M

AU - Oudshoorn, J H

AU - Dorland, L

AU - Berger, R

AU - de Koning, T

PY - 2004

Y1 - 2004

N2 - Resting energy expenditure (REE) was investigated in 8 children with propionic and methylmalonic acidaemias because a lowered REE has been reported in the literature. We observed a marginally elevated REE and think that adequate caloric intake and the use of a synthetic amino acid mixture are responsible for this.

AB - Resting energy expenditure (REE) was investigated in 8 children with propionic and methylmalonic acidaemias because a lowered REE has been reported in the literature. We observed a marginally elevated REE and think that adequate caloric intake and the use of a synthetic amino acid mixture are responsible for this.

KW - Amino Acid Metabolism, Inborn Errors

KW - Amino Acids

KW - Child

KW - Child, Preschool

KW - Drug Combinations

KW - Energy Intake

KW - Energy Metabolism

KW - Female

KW - Humans

KW - Infant

KW - Male

KW - Methylmalonic Acid

KW - Propionates

KW - Journal Article

U2 - 10.1023/B:BOLI.0000016678.78134.7d

DO - 10.1023/B:BOLI.0000016678.78134.7d

M3 - Article

C2 - 15065575

SN - 0141-8955

VL - 27

SP - 111

EP - 112

JO - Journal of Inherited Metabolic Disease

JF - Journal of Inherited Metabolic Disease

IS - 1

ER -

Energy expenditure in patients with propionic and methylmalonic acidaemias

Abstract

Keywords

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