Energy expenditure in patients with propionic and methylmalonic acidaemias

C C van Hagen, E Carbasius Weber, Th A M van den Hurk, J H Oudshoorn, L Dorland, R Berger, T de Koning

Research output: Contribution to journalArticleAcademicpeer-review

9 Citations (Scopus)


Resting energy expenditure (REE) was investigated in 8 children with propionic and methylmalonic acidaemias because a lowered REE has been reported in the literature. We observed a marginally elevated REE and think that adequate caloric intake and the use of a synthetic amino acid mixture are responsible for this.

Original languageEnglish
Pages (from-to)111-112
Number of pages2
JournalJournal of Inherited Metabolic Disease
Issue number1
Publication statusPublished - 2004
Externally publishedYes


  • Amino Acid Metabolism, Inborn Errors
  • Amino Acids
  • Child
  • Child, Preschool
  • Drug Combinations
  • Energy Intake
  • Energy Metabolism
  • Female
  • Humans
  • Infant
  • Male
  • Methylmalonic Acid
  • Propionates
  • Journal Article

Cite this