Living Donor Kidney Transplantation in a Patient With Epidermolysis Bullosa: A Case Report

S. H. E. Ceuppens; H. J. A. N. Kimenai; J. Roodnat; I. R. A. M. Mertens zur Borg; J. C. Duipmans; J. N. M. IJzermans; R. C. Minnee

doi:10.1016/j.transproceed.2019.04.049

Living Donor Kidney Transplantation in a Patient With Epidermolysis Bullosa: A Case Report

S. H. E. Ceuppens, H. J. A. N. Kimenai, J. Roodnat, I. R. A. M. Mertens zur Borg, J. C. Duipmans, J. N. M. IJzermans, R. C. Minnee^*

^*Corresponding author for this work

Research output: Contribution to journal › Article › Academic › peer-review

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Abstract

Severe recessive dystrophic epidermolysis bullosa is a very rare inherited disease with excessive blisters forming starting at birth. Surgical intervention in this population creates a challenge: preventing formation of new lesions while managing previously scarred tissues. We present a case of a 27-year-old patient with end-stage renal disease caused by rapidly progressive IgA nephropathy. Living donor kidney transplantation was performed under local, spinal and epidural anesthesia.

Living kidney transplantation in epidermolysis bullosa patients with end-stage renal disease should not be a contraindication for transplantation and should be considered as a viable and feasible option after careful preparation.

Original language	English
Pages (from-to)	3074-3076
Number of pages	3
Journal	Transplantation Proceedings
Volume	51
Issue number	9
DOIs	https://doi.org/10.1016/j.transproceed.2019.04.049
Publication status	Published - Nov-2019
Externally published	Yes
Event	33rd Spanish Congress of Transplant Coordinators - Seville, Spain Duration: 14-Nov-2018 → 16-Nov-2018

Keywords

RENAL-TRANSPLANT

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10.1016/j.transproceed.2019.04.049

1-s2.0-S0041134519304877-mainFinal publisher's version, 410 KBLicence: Taverne

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@article{1e1441705ebe4ac589c79ae71391a36f,

title = "Living Donor Kidney Transplantation in a Patient With Epidermolysis Bullosa: A Case Report",

abstract = "Severe recessive dystrophic epidermolysis bullosa is a very rare inherited disease with excessive blisters forming starting at birth. Surgical intervention in this population creates a challenge: preventing formation of new lesions while managing previously scarred tissues. We present a case of a 27-year-old patient with end-stage renal disease caused by rapidly progressive IgA nephropathy. Living donor kidney transplantation was performed under local, spinal and epidural anesthesia.Living kidney transplantation in epidermolysis bullosa patients with end-stage renal disease should not be a contraindication for transplantation and should be considered as a viable and feasible option after careful preparation.",

keywords = "RENAL-TRANSPLANT",

author = "Ceuppens, {S. H. E.} and Kimenai, {H. J. A. N.} and J. Roodnat and {zur Borg}, {I. R. A. M. Mertens} and Duipmans, {J. C.} and IJzermans, {J. N. M.} and Minnee, {R. C.}",

year = "2019",

month = nov,

doi = "10.1016/j.transproceed.2019.04.049",

language = "English",

volume = "51",

pages = "3074--3076",

journal = "Transplantation Proceedings",

issn = "0041-1345",

publisher = "ELSEVIER SCIENCE INC",

number = "9",

note = "33rd Spanish Congress of Transplant Coordinators ; Conference date: 14-11-2018 Through 16-11-2018",

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TY - JOUR

T1 - Living Donor Kidney Transplantation in a Patient With Epidermolysis Bullosa

T2 - 33rd Spanish Congress of Transplant Coordinators

AU - Ceuppens, S. H. E.

AU - Kimenai, H. J. A. N.

AU - Roodnat, J.

AU - zur Borg, I. R. A. M. Mertens

AU - Duipmans, J. C.

AU - IJzermans, J. N. M.

AU - Minnee, R. C.

PY - 2019/11

Y1 - 2019/11

N2 - Severe recessive dystrophic epidermolysis bullosa is a very rare inherited disease with excessive blisters forming starting at birth. Surgical intervention in this population creates a challenge: preventing formation of new lesions while managing previously scarred tissues. We present a case of a 27-year-old patient with end-stage renal disease caused by rapidly progressive IgA nephropathy. Living donor kidney transplantation was performed under local, spinal and epidural anesthesia.Living kidney transplantation in epidermolysis bullosa patients with end-stage renal disease should not be a contraindication for transplantation and should be considered as a viable and feasible option after careful preparation.

AB - Severe recessive dystrophic epidermolysis bullosa is a very rare inherited disease with excessive blisters forming starting at birth. Surgical intervention in this population creates a challenge: preventing formation of new lesions while managing previously scarred tissues. We present a case of a 27-year-old patient with end-stage renal disease caused by rapidly progressive IgA nephropathy. Living donor kidney transplantation was performed under local, spinal and epidural anesthesia.Living kidney transplantation in epidermolysis bullosa patients with end-stage renal disease should not be a contraindication for transplantation and should be considered as a viable and feasible option after careful preparation.

KW - RENAL-TRANSPLANT

U2 - 10.1016/j.transproceed.2019.04.049

DO - 10.1016/j.transproceed.2019.04.049

M3 - Article

SN - 0041-1345

VL - 51

SP - 3074

EP - 3076

JO - Transplantation Proceedings

JF - Transplantation Proceedings

IS - 9

Y2 - 14 November 2018 through 16 November 2018

ER -

Living Donor Kidney Transplantation in a Patient With Epidermolysis Bullosa: A Case Report

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