Myotonia and flaccid dysarthria in patients with adult onset myotonic dystrophy

B. J.M. de Swart*, B. G.M. van Engelen, J. P.B.M. van de Kerkhof, B. A.M. Maassen

*Bijbehorende auteur voor dit werk

Onderzoeksoutput: ArticleAcademicpeer review

15 Citaten (Scopus)
3 Downloads (Pure)


Background: Myotonia and weakness are the most important components of dysarthric speech in myotonic dystrophy.

Objective: To specify and quantify possible defects in speech execution in patients with adult onset myotonic dystrophy.

Methods: Studies on speech production were done on 30 mildly affected patients with myotonic dystrophy. Special attention was paid to myotonia. Because muscle activity can result in a decrease of myotonia, speech characteristics were measured before and after warm up. The possibility that warming up causes increased weakness was also assessed.

Results: As with other motor skills, a warm up effect was found in speech production, resulting in an increase in repetition rate and a decrease in variability of repetition rate. Signs of fatigue did not occur.

Conclusions: Warming up is valuable for patients with myotonic dystrophy in reducing the influence of myotonia on speech production.

Originele taal-2English
Pagina's (van-tot)1480-1482
Aantal pagina's3
TijdschriftJournal of Neurology, Neurosurgery and Psychiatry
Nummer van het tijdschrift10
StatusPublished - okt.-2004
Extern gepubliceerdJa

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